| Agent | Responses |
| | 4 |
| (-)-OSU6162 (Pharmacia & Upjohn) | 1 |
| (-)-PHCCC | 1 |
| (†)KW-6002 | 1 |
| (specific peptides) | 3 |
| †estrogen | 1 |
| †GM-1 ganglioside (Fidia) | 2 |
| †GPI-1485 (Guilford) | 2 |
| †nicotine | 2 |
| †pramipexole (also †ropinirole) | 2 |
| †rasagiline (Teva) | 1 |
| †selegiline | 2 |
| 2-methyl-6-(phenylethynyl)-pyridine (MPEP) | 1 |
| 2-MPPA | 1 |
| 4-chlorokinurenine | 2 |
| ACR-16 | 1 |
| ACR16 (4-(3-Methanesulfonyl-phenyl)-1-propylpiperidine ) | 1 |
| Activin A | 2 |
| adenosine | 1 |
| adenosine amine congener (ADAC) | 1 |
| adrenoceptor blockade | 2 |
| AEOL10113 | 2 |
| AEOL10113, AEOL10150 | 1 |
| AEOL10150 | 1 |
| AIT-082 (Neotrofin) | 1 |
| AM404 | 1 |
| Amantadine | 2 |
| anthocyanins | 2 |
| Apomorphine | 1 |
| AR-A014418 | 1 |
| Ariflo (cilomilast, SB 207499) SmithKline | 1 |
| aripiprazole (OPC-14597; Abilify; Otsuka/BMS) | 1 |
| Ascorbic Acid | 3 |
| AV-101 (VistaGen) | 1 |
| Baclofen | 1 |
| BCTC (Purdue Pharma) | 2 |
| BDNF | 1 |
| Benzothiazoles | 1 |
| bFGF | 1 |
| bivalent peptide | 1 |
| BN-82451 | 4 |
| bpV[phen] | 1 |
| bromocriptine | 4 |
| BRX-220 (bimoclomol) | 1 |
| bupropion (Wellbutrin; Zyban) | 1 |
| cabergoline | 1 |
| Cannabinoids | 4 |
| carboxyfullerene | 1 |
| cardiac glycosides, specifically: digoxin, digitoxin, peruvoside and nerifolin | 1 |
| celastrol | 1 |
| CEP-1347 | 2 |
| CGS 15943 | 1 |
| chloroquine | 1 |
| citicoline | 1 |
| clioquinol | 1 |
| Clozapine | 2 |
| CNTF (Axokine) | 2 |
| Coenzyme Q10 | 3 |
| Combination Therapy | 1 |
| Congo Red | 6 |
| copolymer 1 | 2 |
| CP101606 | 1 |
| CPCCOEt | 2 |
| Creatine | 3 |
| CSC | 1 |
| Cyclosporin | 1 |
| Cystamine | 4 |
| Cysteamine | 1 |
| DATN | 2 |
| DCA | 3 |
| desipramine (Norpramine, Pertofrane) | 2 |
| Dextromethorphan | 2 |
| DFMO | 1 |
| DHA (docosahexaeonic acid) | 1 |
| DHEA | 1 |
| DHPG | 1 |
| dibenzomethane | 1 |
| Dichloroacetate | 1 |
| efaroxan | 1 |
| Eliprodil | 1 |
| Enoxaparin (Lovenox) | 2 |
| Ergot | 3 |
| erythropoeitin | 1 |
| essential fatty acid mixture | 1 |
| Essential Fatty Acids | 1 |
| estrogen | 3 |
| Ethyl Eicosapentaenoate (LAX-101) | 2 |
| EUK-189 & -207 (Eukarion, Inc.) | 1 |
| exelon | 1 |
| fatty acids | 2 |
| Fetal cells (Porcine) | 2 |
| Fetal striatal (allograft) | 1 |
| Fetal Striatal (Human) | 1 |
| flavopiridol | 2 |
| fluoxetine | 3 |
| Fluoxetine (commonly marketed as Prozac) | 1 |
| flurbiprofen | 3 |
| galantamine (Reminyl) J&J, Shire | 1 |
| gamma-vinyl GABA | 2 |
| GDNF | 2 |
| GDNF/Neurturin | 1 |
| Geldanamycin | 2 |
| geldanamycin (& herbimycinA?) | 2 |
| gene knock-down | 1 |
| genistein | 2 |
| Geranylgeranylacetone | 1 |
| Ginkgo biloba extract EGb761 | 1 |
| ginseng | 2 |
| Glyconutrient compound, Phytonutrient compound, PhytoSterols, and Vitamins and Minerals | 1 |
| Glyconutrients | 3 |
| GM-1 ganglioside (Fidia) | 1 |
| GPE | 1 |
| GPI-1485 (Guilford) | 1 |
| GW5074 ({5-Iodo-3-[(3,5-dibromo-4-hydroxyphenyl) methylene]-2-indolinone} | 1 |
| HCT-1026(NicOx [France]) | 1 |
| histone acetylase inhibitor | 1 |
| HT0712 | 1 |
| htt antibodies | 2 |
| HU211 dexanabinol (+)enantiomer | 1 |
| Human umbilical cells | 1 |
| ibudilast | 1 |
| Idebenone | 2 |
| Ifenprodil | 2 |
| IL-6 | 1 |
| indomethacin | 1 |
| isoniazid | 1 |
| JNK inhibitors | 1 |
| Ketamine | 1 |
| KP544 (Krenitsky Phar) | 1 |
| KW-6002 | 2 |
| L-arginyl-3,4-spermidine | 1 |
| lamotrigine (Glaxo) | 3 |
| levetiracetam (Keppra, UCB Pharma) | 1 |
| Lipator | 2 |
| Lipoic Acid | 2 |
| lisuride | 2 |
| Lithium | 2 |
| lithium (chloride) | 2 |
| LY294002 | 1 |
| LY341495 (Lilly) | 3 |
| LY354740 (Lilly) | 2 |
| LY366457 | 1 |
| LY379268 (Lilly) | 2 |
| M40403 (MetaPhore Ph) | 1 |
| M826 (Merck-Frosst) | 2 |
| many | 2 |
| Maprotiline (Ludiomil) | 2 |
| Melatonin | 2 |
| Memantine | 2 |
| mGluR2 agonist LY379268 | 2 |
| milacemide | 1 |
| Minocycline | 3 |
| Mithramycin | 1 |
| mitoquinone | 2 |
| N-acetyl-L-cysteine | 2 |
| NAAG | 1 |
| NCX-2216(NicOx [France]) | 1 |
| neramexane Forest Lab, NYC Merz Pharma, Germany | 3 |
| Neurotrophins | 1 |
| neurterin | 1 |
| NGF | 1 |
| nicaraven | 2 |
| nicotine | 3 |
| nimodipine | 1 |
| NN-DNJ | 1 |
| nNOS inhibitors (presymptomatic); nitric oxide donors (symptomatic) | 1 |
| NO modulation | 1 |
| Nortriptyline (Aventyl, Pamelor) | 1 |
| NR2B antagonists such as Ifenprodil | 2 |
| NS-398 (Cayman Chemical) | 2 |
| NT4/5 | 1 |
| NVP-ABE171 Novartis | 2 |
| NW-1029 | 1 |
| NXY 059 | 1 |
| olanzapine | 2 |
| olanzapine (Zyprexa; Lilly) | 1 |
| OPC-14117 | 1 |
| orexins (hypocretins) | 2 |
| oxcarbazepine (Trileptal, Novartis) | 1 |
| paroxetine (Paxil) | 1 |
| PD150606 (Calbiochem) | 2 |
| pergolide | 1 |
| Phenylbutyrate | 2 |
| phosphono-phenylglycine | 1 |
| pimagedine (Altheon) | 1 |
| PN401 | 1 |
| pramipexole (also ropinirole) | 1 |
| pregnenolone (sulfate) | 1 |
| prinomastat | 2 |
| Propranolol (Inderal LA) | 1 |
| Pyroxamide | 1 |
| Pyruvate | 1 |
| QBP1 (polyglutamine (Q) Binding Peptide 1) | 2 |
| quinacrine (hydrocholoride) | 2 |
| rapamycin | 1 |
| rasagiline (Teva) | 1 |
| Remacemide | 3 |
| resveratrol | 2 |
| Riluzole | 3 |
| RNAi- interfering RNA | 3 |
| Ro256981 | 1 |
| ROCK Inhibitors p160 (Y-27632) | 4 |
| rolipram | 2 |
| RU486 (mifepristone) | 3 |
| S 17092 | 1 |
| SB-415286 Glaxo SmithKline | 1 |
| SB203580 (Calbiochem) | 1 |
| SC58125 (Monsanto?) | 3 |
| SCH58261 (Schering) | 1 |
| selegiline | 1 |
| SJA6017 (Pfizer) | 1 |
| SKF-38393 (SmithKline) | 1 |
| sodium butyrate | 3 |
| ST 198 (patented – who?) | 3 |
| SU6656 | 3 |
| Suberoylanilide hydroxamic acid (SAHA) | 2 |
| Sulpiride | 1 |
| Tacrolimus (also FK-506 or Fujimycin) | 5 |
| Tat-NR2B9c | 1 |
| Tauroursodeoxycholic acid (TUDCA) | 3 |
| terguride | 2 |
| Test by Eric Morrie | 1 |
| tetrabenazine | 1 |
| TGFa | 3 |
| thapsigargin | 2 |
| THIP | 2 |
| Tiapride | 1 |
| TMAO | 1 |
| TPA | 1 |
| Trehalose | 4 |
| troglitazone | 1 |
| Troglitizones | 1 |
| tubacin | 1 |
| TUDCA | 1 |
| TV3326 (Teva) | 1 |
| U0126 | 1 |
| UCM707 | 1 |
| UDCA - Ursodial | 1 |
| Ursodiol UDCA | 1 |
| Valproate | 2 |
| verapamil | 1 |
| Vitamin E | 1 |
| VK-28 | 1 |
| WHI-P131 | 1 |
| Wild type htt | 1 |
| WIN55,212-2 (Lilly) | 1 |
| Y-27632 | 2 |
| z-VAD-fmk | 1 |
| ziprasidone | 2 |
| ZK 216348 (Schering AG) | 2 |
| ZK200775 (Eisai) | 1 |